We describe two cases of Reactive Hemophagocytic syndrome (RHS) occurring in rheumatic diseases in childhood. Patient 1, an adolescent girl with systemic onset Juvenile idopathic arthritis (JRA) presented like severe sepsis with shock, hepatic dysfunction and coagulopathy. Patient 2 presented with cardiac tamponade, she was later detected to have systemic lupus erythematosus (SLE). Her bone marrow aspirate revealed prominent hemophagocytosis. Both cases improved with pulse methylprednisolone therapy. © 2008 Dr. K C Chaudhuri Foundation.
cited By (since 1996)2
La Rajam, Prasad, Vab, and Yatheesha, B. La, “Reactive Hemophagocytic syndrome”, Indian Journal of Pediatrics, vol. 75, pp. 1261-1263, 2008.