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Moyamoya Disease Associated With Hereditary Spherocytosis

Publication Type : Journal Article

Thematic Areas : Medical Sciences

Publisher : Neurol India

Source : Neurol India, Volume 66, Number 4 (2018)

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Campus : Kochi

School : School of Medicine

Department : Neurology

Year : 2018

Abstract : A 5-year-old girl with hereditary spherocytosis presented with two episodes of transient ischemic attacks within a month. Cranial magnetic resonance imaging angiography revealed a left internal carotid artery and middle cerebral artery stenosis, with an extensive vascular mesh in the thalamic area indicative of moyamoya disease. Treatment consisted of supporting cerebral perfusion with blood transfusions, and splenectomy to prevent recurrence. Moyamoya disease is a very unusual cerebrovascular disorder in childhood and its association with hereditary spherocytosis is rarely reported.

Cite this Research Publication : Dr. Saraf Udit Umesh, Arun K., Sreedharan S. E., Rajalakshmi P., and Sylaja P. N., “Moyamoya Disease Associated With Hereditary Spherocytosis”, Neurol India, vol. 66, 2018.

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