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Systemic onset juvenile idiopathic arthritis with macrophage activation syndrome misdiagnosed as Kawasaki disease: case report and literature review

Publication Type : Journal Article

Thematic Areas : Medical Sciences

Publisher : Rheumatology International

Source : Rheumatology International, p.1-5 (2010)

Url : http://www.scopus.com/inward/record.url?eid=2-s2.0-78649546470&partnerID=40&md5=387c19c4ff7d27b0fb17252818d11d50

Campus : Kochi

School : School of Medicine

Department : Paediatric Cardiology

Year : 2010

Abstract : Patients with systemic onset juvenile idiopathic arthritis (SoJIA) are rarely known to develop coronary artery dilatation. The American heart association (AHA) statement on evaluation of suspected Kawasaki disease (KD) would lead some SoJIA patients (particularly in the early stages of the disease) to be inaccurately classified as KD. In addition to the institution of inappropriate therapy with IVIG, misdiagnosis as KD can delay definitive treatment for these SoJIA patients who probably have a worse predicted outcome. We present a 6-year-old male patient with SoJIA who was initially classified as incomplete KD. The child developed life-threatening macrophage activation syndrome (MAS). Previous literature regarding coronary dilatation in SoJIA is also reviewed. © 2010 Springer-Verlag.

Cite this Research Publication : Sa Kumar, Vaidyanathan, Bb, Gayathri, Sc, and Rajam, Lc, “Systemic onset juvenile idiopathic arthritis with macrophage activation syndrome misdiagnosed as Kawasaki disease: case report and literature review”, Rheumatology International, pp. 1-5, 2010.

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