Rosai Dorfman disease (RDD), also known as sinus histiocytosis with massive lymphadenopathy, is a benign histiocytic proliferative disorder mainly affecting the lymph nodes. Although several cases of extra-nodal involvement have been reported previously, central nervous system involvement, particularly in the absence of nodal disease is extremely rare. We report a case of isolated intracranial RDD occurring in a relatively elder patient, which was shown by histological examination to have a dura-based involvement.
cited By (since 1996)2
Va Krishnamoorthy, Parmar, C. Fb, and Panikar, Da, “Isolated intracranial Rosai Dorfman disease”, Neurology India, vol. 59, pp. 443-446, 2011.